Pediatric Chiari malformation Type 0: a 12-year institutional experience.

@article{Chern2011PediatricCM,
  title={Pediatric Chiari malformation Type 0: a 12-year institutional experience.},
  author={Joshua J. Chern and Amber Gordon and Martin M. Mortazavi and R. Shane Tubbs and Walter Jerry Oakes},
  journal={Journal of neurosurgery. Pediatrics},
  year={2011},
  volume={8 1},
  pages={
          1-5
        }
}
OBJECT In 1998 the authors identified 5 patients with syringomyelia and no evidence of Chiari malformation Type I (CM-I). Magnetic resonance imaging of the entire neuraxis ruled out other causes of a syrinx. Ultimately, abnormal CSF flow at the foramen magnum was the suspected cause. The label "Chiari 0" was used to categorize these unique cases with no tonsillar ectopia. All of the patients underwent posterior fossa decompression and duraplasty identical to the technique used to treat patients… 

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