Pathophysiology of idiopathic dystonia: findings from genetic animal models

@article{Richter1998PathophysiologyOI,
  title={Pathophysiology of idiopathic dystonia: findings from genetic animal models},
  author={Angelika Richter and Wolfgang L{\"o}scher},
  journal={Progress in Neurobiology},
  year={1998},
  volume={54},
  pages={633-677}
}
Alternative Approaches to Modeling Hereditary Dystonias
TLDR
It was found that partial selective pharmacological block of the sodium pumps in the cerebellum and basal ganglia of mice recapitulates all of the salient features of DYT12, including dystonia and parkinsonism induced by stress.
Dystonia and the cerebellum: A new field of interest in movement disorders?
The functional neuroanatomy of dystonia
Experimental therapeutics for dystonia
Rodent models for dystonia research: Characteristics, evaluation, and utility
TLDR
A recent workshop addressed four main issues affecting those who conduct dystonia research with animal models, including the different ways in which dystonic disorders can be modeled in rodents, key features that constitute a useful model, methods used in the evaluation of these models, and recommendations for future research.
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