Pathology of the liver in mucopolysaccharidosis: light and electron microscopic assessment before and after bone marrow transplantation.

@article{Resnick1992PathologyOT,
  title={Pathology of the liver in mucopolysaccharidosis: light and electron microscopic assessment before and after bone marrow transplantation.},
  author={Jeffrey M. Resnick and William Krivit and DaleC. Snover and John H. Kersey and Norma K. C. Ramsay and Bruce R Blazar and Chester B. Whitley},
  journal={Bone marrow transplantation},
  year={1992},
  volume={10 3},
  pages={
          273-80
        }
}
Serial liver biopsies were obtained in 20 patients undergoing bone marrow transplantation (BMT) for mucopolysaccharidosis (MPS). The 13 patients with MPS I, one with MPS II, four with MPS III, and two with MPS VI underwent liver biopsy prior to and from 1 to 37 months after BMT. The amount of accumulated glycosaminoglycan (GAG) was assessed by semiquantitation of Kupffer cell staining with colloidal iron and by counting the number of hepatocellular GAG-containing lysosomes in electron… CONTINUE READING

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