Paroxysmal nocturnal hemoglobinuria in Budd-Chiari syndrome: findings from a cohort study.

  title={Paroxysmal nocturnal hemoglobinuria in Budd-Chiari syndrome: findings from a cohort study.},
  author={Jildou Hoekstra and Frank W G Leebeek and Aur{\'e}lie Plessier and Sebasti{\'a}n R Raffa and Sarwa Darwish Darwish Murad and Joerg Heller and Antoine Hadengue and Carine Chagneau and Elwyn E Elias and Massimo Primignani and Juan Carlos Garc{\'i}a-Pag{\'a}n and Dominique Charles Valla and Harry L. A. Janssen},
  journal={Journal of hepatology},
  volume={51 4},
BACKGROUND/AIMS A well recognized cause of Budd-Chiari syndrome (BCS) is paroxysmal nocturnal hemoglobinuria (PNH). PNH is an acquired disorder of hematopoietic stem cells, characterized by intravascular hemolysis and venous thrombosis. Testing for this hematological disorder should be considered in all BCS patients. METHODS Using data from the EN-Vie study, a multi-center study of 163 patients with BCS, we investigated the relationship between BCS and PNH in 15 patients with combined disease… CONTINUE READING
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Prospective follow-up study on 163 patients with Budd-Chiari syndrome: results from the European network for vascular disorders of the liver (EN-VIE)

  • SD Murad, A Plessier, M Hernandez-Guerra, M Primignani, E Elias, M Bahr
  • J Hepatol 2007;46:S4
  • 2007
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