Paraneoplastic Brain Stem Encephalitis
@article{Blaes2013ParaneoplasticBS, title={Paraneoplastic Brain Stem Encephalitis}, author={Franz Blaes}, journal={Current Treatment Options in Neurology}, year={2013}, volume={15}, pages={201-209} }
Opinion statementParaneoplastic brain stem encephalitis can occur as an isolated clinical syndrome or, more often, may be part of a more widespread encephalitis. Different antineuronal autoantibodies, such as anti-Hu, anti-Ri, and anti-Ma2 can be associated with the syndrome, and the most frequent tumors are lung and testicular cancer. Anti-Hu-associated brain stem encephalitis does not normally respond to immunotherapy; the syndrome may stabilize under tumor treatment. Brain stem encephalitis…
16 Citations
Paraneoplastic Brainstem Encephalitis Associated with Anti-Hu Antibody
- Medicine, Biology
- 2015
A 79-year-old man who suddenly developed memory loss, diplopia and cerebellar ataxia is reported with acute-onset of paraneoplastic brainstem encephalitis with anti-Hu antibody.
Anti-Ma2-Associated Encephalitis Secondary to Hodgkin’s Lymphoma
- Medicine, BiologyCanadian Journal of Neurological Sciences / Journal Canadien des Sciences Neurologiques
- 2017
The first case associated with HL is reported in a 60-year-old male presenting with neuropsychiatric symptoms, cataplexy, hypoglycemic episodes, and vertical supranuclear gaze palsy (VSGP), which involves a man with a 25-year history of well-controlled epilepsy.
Anti-Ma 2-Associated Encephalitis Secondary to Hodgkin ’ s Lymphoma Keywords : Hodgkin ’ s lymphoma , Paraneoplastic syndrome
- Medicine, Biology
- 2017
The first case associated with HL is reported in a 60-year-old male presenting with neuropsychiatric symptoms, cataplexy, hypoglycemic episodes, and vertical supranuclear gaze palsy (VSGP) in a man with a 25-year history of well-controlled epilepsy.
Paraneoplastic Diseases of the Central Nervous System
- Medicine, BiologyF1000Research
- 2020
Paraneoplastic neurological syndromes are nonmetastatic complications of malignancy secondary to immune-mediated neuronal dysfunction or death. Pathogenesis may occur from cell surface binding of…
Paraneoplastic immune-mediated neurological effects of systemic cancers
- MedicineExpert review of clinical immunology
- 2014
Effective therapy of the primary cancer consists the best current therapy for a given paraneoplastic syndrome, however, other forms of immune modulation, such as plasma exchange, intravenous gamma globulin, other immune therapies and symptomatic treatment for certain PNS may have additional benefit.
Brainstem Encephalitis. The Role of Imaging in Diagnosis.
- MedicineCurrent problems in diagnostic radiology
- 2020
The imaging presentation of BE is reviewed with the help of case examples and it is shown that clinical presentation, the spatial distribution of lesions, and other associated radiological lesions can provide the radiologists and clinician the clues to an accurate diagnosis.
Trismus caused by paraneoplastic brainstem encephalitis
- MedicinePractical Neurology
- 2018
The assessment and differential diagnoses of a middle-aged man who presented with trismus, double vision and behavioural problems, and suspected a paraneoplastic brainstem encephalitis, who is currently undergoing treatment with chemotherapy and radiotherapy.
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