Paranasal sinuses chordoma is rare in pediatric patients. We report a case of a 15-month-old patient who presented with a nasal mass, accompanied by gradual nasal obstruction since 3 months of age. A 3.2 cmx2.2 cmx3.0 cm neoplasm was found in left maxillary sinus, ethmoid sinus and nasal cavity by CT scans. Surgery was performed through endonasal endoscopic approach under general anesthesia. Both histological examination of the biopsy and the tissue removed by surgery revealed a chordoma. No tumor has recurred during the 3-year follow-up. With total removal of the tumor, the endonasal endoscope is a safe approach with facial features remaining undestroyed.