Papillary glioneuronal tumor—a rare entity: report of four cases and brief review of literature

@article{Agarwal2012PapillaryGT,
  title={Papillary glioneuronal tumor—a rare entity: report of four cases and brief review of literature},
  author={Shipra Agarwal and Mehar Chand Sharma and Geetika Singh and Vaishali Suri and Chitra Sarkar and Ajay Garg and Rajinder Kumar and P. Sharat Chandra},
  journal={Child's Nervous System},
  year={2012},
  volume={28},
  pages={1897-1904}
}
PurposePapillary glioneuronal tumors (PGNT) have been recently included as a distinct entity in the WHO classification of tumors of the central nervous system. Their molecular pathogenesis is not clear. In the current study, we present the morphological, immunohistochemical, and molecular features of four cases of PGNT reported over the past 11 years.MethodsOver a period of 11 years (January 2000–February 2010), there were four cases of PGNT, which were reviewed for histomorphological features… 

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TLDR
It is reinforced that PGNTs are tumors that usually occur in young adults and are cystic/solid, supratentorial, closely located with the ventricle, molecularly genetically different from astrocytic or oligodendroglial tumors, and indolent in behavior.
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TLDR
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