Panostotic Fibrous Dysplasia: A New Craniotubular Dysplasia

  title={Panostotic Fibrous Dysplasia: A New Craniotubular Dysplasia},
  author={William D. Leslie and Caroline Reinhold and L{\'e}onard Rosenthall and C Tau and Francis H. Glorieux},
  journal={Clinical Nuclear Medicine},
The authors describe the radiographic-scintigraphic features of an unusual craniotubular dysplasia characterized by diffuse osteopenia with bone expansion and a “ground glass” appearance, markedly increased skeletal turnover, myelofibrosis, hypophosphatemia, and pigmented “coast-of-Maine” patches. This syndrome, termed panostotic fibrous dysplasia, is distinct from previously reported disorders. 
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