Outcome of goal-directed non-invasive ventilation and mechanical insufflation/exsufflation in spinal muscular atrophy type I

@article{Chatwin2010OutcomeOG,
  title={Outcome of goal-directed non-invasive ventilation and mechanical insufflation/exsufflation in spinal muscular atrophy type I},
  author={Michelle Chatwin and Andrew Bush and Anita Simonds},
  journal={Archives of Disease in Childhood},
  year={2010},
  volume={96},
  pages={426 - 432}
}
Background There are widely discrepant views on the respiratory management of infants with spinal muscular atrophy (SMA) type I. Typically, management is palliative. Design A descriptive study of interventions and investigations is reported that were offered to a cohort of 13 children with SMA type I referred to our centre. Interventions and investigations included sleep studies, provision of non-invasive positive pressure ventilation (NIPPV) for ventilatory support/dependency and for… 
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