Osteogenesis Imperfecta Surgical Management of the Femur and Knee

  title={Osteogenesis Imperfecta Surgical Management of the Femur and Knee},
  author={Paul William Esposito and Maegen Wallace},
Osteogenesis imperfecta (OI) has a wide range of presentations and oftentimes presents with recurrent femur fractures and/or significant femoral bowing. The concern with femoral bowing is that as children begin to pull to stand, weight bear, cruise, and walk, they are at an increased risk of femur fractures as there are significant tension stresses across the bowed area. Femur fractures, no matter the age or underlying diagnosis, are extremely painful, and in our opinion, avoiding these… 


Elastic stable intramedullary nailing of femoral shaft fractures in children.
Compared with conservative treatment, ESIN obviates the need for prolonged bed rest and is thus particularly advantageous for treating children, and early weight-bearing is possible and is recommended.
Mid-term Results of Femoral and Tibial Osteotomies and Fassier-Duval Nailing in Children With Osteogenesis Imperfecta
This series lends evidence to the medium-term utility of FD intramedullary rods as an effective and less invasive platform for stabilization and correction of deformity in long bones of patients with OI.
Surgical treatment of osteogenesis imperfecta: current concepts
Treatment indications and choices of surgical techniques based on recent clinical studies are outlined, in addition to identifying persistent clinical problems addressed in recent literature.
Sandwich allografts for long-bone nonunions in patients with osteogenesis imperfecta: a retrospective study.
Sandwich allograft struts constitute a durable, safe method for the stabilization and healing of persistent long-bone nonunions in patients with osteogenesis imperfecta.
Locking plate placement with unicortical screw fixation adjunctive to intramedullary rodding in long bones of patients with osteogenesis imperfecta.
Unicortical locking plate fixation effectively supplements intramedullary rod fixation in selected cases of osteogenesis imperfecta.
Intramedullary nailing with supplemental plate and screw fixation of long bones of patients with osteogenesis imperfecta: operative technique and preliminary results
Although further follow-up and investigation will provide further insight into long-term outcomes, supplemental plate and screw fixation is a valuable and versatile option for this challenging patient population.
Fassier-Duval Telescopic System: How I Do It?
  • F. Fassier
  • Medicine
    Journal of pediatric orthopedics
  • 2017
The author describes step-by-step the technique for Fassier-Duval rodding of both femurs and tibiae in osteogenesis imperfecta and emphasis is given on the different tricks to avoid intraoperative problems.
Anesthesia in children with osteogenesis imperfecta: Retrospective chart review of 83 patients and 205 anesthetics over 7 years
Osteogenesis imperfecta is the collective term for a heterogeneous group of connective tissue syndromes characterized by bone fragility with multisystem involvement and perioperative implications.
Osteogenesis imperfecta.
Further investigation is needed urgently to identify forms of medical therapy that will decrease morbidity in osteogenesis imperfecta.