Orthopaedic management of the Ehlers–Danlos syndromes

  title={Orthopaedic management of the Ehlers–Danlos syndromes},
  author={William B. Ericson and Roger L. Wolman},
  journal={American Journal of Medical Genetics Part C: Seminars in Medical Genetics},
  pages={188 - 194}
  • W. EricsonR. Wolman
  • Published 1 March 2017
  • Medicine
  • American Journal of Medical Genetics Part C: Seminars in Medical Genetics
The role of orthopedic surgery in Ehlers–Danlos syndrome is inherently controversial, opaque to most patients and many medical providers, and difficult to discern from available medical literature. Non‐operative treatment is preferable, but for carefully selected patients, specific joint stabilization and nerve decompression procedures can provide symptomatic relief when conservative measures fail. © 2017 Wiley Periodicals, Inc. 

Perioperative Care in Patients with Ehlers Danlos Syndromes

Patients with Ehlers Danlos Syndromes may present with an array of coexisting medical conditions such as Dysautonomia, Mast Cell Activation Syndrome, Chiari Malformation, Tethered Cord Syndrome, Craniocervical instability, Gastroparesis, altered sensitivity to local anesthetics.

[Ehlers-Danlos syndrome].

The aim of this article is to provide an overview of the clinical symptoms of Ehlers-Danlos syndrome and to provide recommendations on diagnosis and treatment.

Shoulder Arthroplasty is a Viable Option in Patients with Ehlers-Danlos Syndrome.

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Thirteen EDS subtypes are recognized, with a wide degree of symptom overlap among subtypes and with other connective tissue disorders.

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Pain management in the Ehlers–Danlos syndromes

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A multidisciplinary approach to the diagnosis of the patient, including clinical and molecular analysis, and neuropsychological and psychological assessment, is important to improve the treatment choice and the outcome prediction of the patients.



Joint surgery in Ehlers-Danlos patients: results of a survey.

The population surveyed in the present study demonstrates that problems of surgical procedures in EDS may be high relative to other populations without connective-tissue disorders.

Ehlers-Danlos Syndrome in Orthopaedics

It is important to accurately identify patients with Ehlers-Danlos syndrome to initiate appropriate musculoskeletal treatment, optimize anesthetic and postoperative management, perform appropriate vascular screening, and help families address their concerns with other families and advocacy groups.

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This review supports treating colon perforations in EDS-IV patients with TAC and end ileostomy to avoid a reperforation or an anastamotic leak.

Tendinopathies of the Hand and Wrist

Tendinopathies involving the hand and wrist are common. Many are diagnosed easily, and in many cases, the management is straightforward, provided the pathology and principles are understood. Common

Greater Trochanteric Pain Syndrome

The present understanding of the lesions that comprise GTPS is reviewed, discussing the relevant anatomy, diagnostic workup and recommended treatment for trochanteric bursitis, gluteus medius and minimus tears, and external coxa saltans.

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The possibility of resistance to local anaesthesia in individuals with this common and under-diagnosed condition is drawn to draw attention to.

Inferior capsular shift for involuntary inferior and multidirectional instability of the shoulder. A preliminary report.

In thirty-six patients (forty shoulders) with involuntary inferior and multidirectional subluxation and dislocation, there had been failure of standard operations or uncertainty regarding diagnosis or treatment, there have been no other unsatisfactory results to date.

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Ehlers-Danlos syndrome, hypermobility type, constituting a phenotypic continuum with or, perhaps, corresponding to the joint hypermobility syndrome (JHS/EDS-HT), is likely the most common, though the

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