Orthopaedic management of the Ehlers–Danlos syndromes

@article{Ericson2017OrthopaedicMO,
  title={Orthopaedic management of the Ehlers–Danlos syndromes},
  author={William B. Ericson and Roger L. Wolman},
  journal={American Journal of Medical Genetics Part C: Seminars in Medical Genetics},
  year={2017},
  volume={175},
  pages={188 - 194}
}
  • W. Ericson, R. Wolman
  • Published 1 March 2017
  • Medicine
  • American Journal of Medical Genetics Part C: Seminars in Medical Genetics
The role of orthopedic surgery in Ehlers–Danlos syndrome is inherently controversial, opaque to most patients and many medical providers, and difficult to discern from available medical literature. Non‐operative treatment is preferable, but for carefully selected patients, specific joint stabilization and nerve decompression procedures can provide symptomatic relief when conservative measures fail. © 2017 Wiley Periodicals, Inc. 

Perioperative Care in Patients with Ehlers Danlos Syndromes

TLDR
Patients with Ehlers Danlos Syndromes may present with an array of coexisting medical conditions such as Dysautonomia, Mast Cell Activation Syndrome, Chiari Malformation, Tethered Cord Syndrome, Craniocervical instability, Gastroparesis, altered sensitivity to local anesthetics.

[Ehlers-Danlos syndrome].

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Shoulder Arthroplasty is a Viable Option in Patients with Ehlers-Danlos Syndrome.

A review of Ehlers-Danlos syndrome.

TLDR
Thirteen EDS subtypes are recognized, with a wide degree of symptom overlap among subtypes and with other connective tissue disorders.

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TLDR
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Pain management in the Ehlers–Danlos syndromes

TLDR
Management strategies for chronic pain in EDS includes physical therapy, medications, as well as durable medical equipment such as cushions, compressive garments, and braces, which are discussed in this paper.

Bilateral Acromioclavicular Joint Subluxation in an Adolescent with Ehlers-Danlos Syndrome: Case Report and Literature Review

TLDR
The case of a 15-year-old male with Ehlers-Danlos syndrome who presented with complaints of subsequent nontraumatic bilateral ACJ subluxations and pain and ACJ reconstruction via an open mini-Mumford procedure is presented.

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