Orthopaedic management of the Ehlers–Danlos syndromes

@article{Ericson2017OrthopaedicMO,
  title={Orthopaedic management of the Ehlers–Danlos syndromes},
  author={William B. Ericson and Roger L. Wolman},
  journal={American Journal of Medical Genetics Part C: Seminars in Medical Genetics},
  year={2017},
  volume={175},
  pages={188 - 194}
}
  • W. EricsonR. Wolman
  • Published 1 March 2017
  • Medicine
  • American Journal of Medical Genetics Part C: Seminars in Medical Genetics
The role of orthopedic surgery in Ehlers–Danlos syndrome is inherently controversial, opaque to most patients and many medical providers, and difficult to discern from available medical literature. Non‐operative treatment is preferable, but for carefully selected patients, specific joint stabilization and nerve decompression procedures can provide symptomatic relief when conservative measures fail. © 2017 Wiley Periodicals, Inc. 

Perioperative Care in Patients with Ehlers Danlos Syndromes

Patients with Ehlers Danlos Syndromes may present with an array of coexisting medical conditions such as Dysautonomia, Mast Cell Activation Syndrome, Chiari Malformation, Tethered Cord Syndrome, Craniocervical instability, Gastroparesis, altered sensitivity to local anesthetics.

[Ehlers-Danlos syndrome].

The aim of this article is to provide an overview of the clinical symptoms of Ehlers-Danlos syndrome and to provide recommendations on diagnosis and treatment.

Shoulder Arthroplasty is a Viable Option in Patients with Ehlers-Danlos Syndrome.

A review of Ehlers-Danlos syndrome.

Thirteen EDS subtypes are recognized, with a wide degree of symptom overlap among subtypes and with other connective tissue disorders.

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Although this study is able to identify positive and negative trends with certain modalities, it is vital to understand that EDS is not a uniform diagnosis among patients, and that a combination of several different treatments usually is needed for optimal symptom control.

Pain management in the Ehlers–Danlos syndromes

Management strategies for chronic pain in EDS includes physical therapy, medications, as well as durable medical equipment such as cushions, compressive garments, and braces, which are discussed in this paper.

Ehlers-Danlos: A Literature Review and Case Report in a Colombian Woman with Multiple Comorbidities

A multidisciplinary approach to the diagnosis of the patient, including clinical and molecular analysis, and neuropsychological and psychological assessment, is important to improve the treatment choice and the outcome prediction of the patients.

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