Oral and genital ulceration: a unique presentation of immunodeficiency in Athabascan-speaking American Indian children with severe combined immunodeficiency.

@article{Kwong1999OralAG,
  title={Oral and genital ulceration: a unique presentation of immunodeficiency in Athabascan-speaking American Indian children with severe combined immunodeficiency.},
  author={Paul C. Kwong and A S O'Marcaigh and Ren{\'e}e M Howard and Morton J. Cowan and Ilona J Frieden},
  journal={Archives of dermatology},
  year={1999},
  volume={135 8},
  pages={
          927-31
        }
}
BACKGROUND Oral and genital ulcerations have been previously reported in 3 Navajo children diagnosed with severe combined immunodeficiency disease with T- and B-cell lymphopenia (T-B(-)-SCID). OBJECTIVE To evaluate the occurrence of oral and genital ulcerations in 12 Athabascan-speaking American Indians with a diagnosis of T-B(-)-SCID (SCIDA group) and to compare their occurrence in non-Athabascan-speaking children with SCID (control group). We also observed the course of these ulcerations in… 

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