Nutritional value of essential amino acids in the treatment of adults with phenylketonuria

Abstract

The present short-term N-balance study in adult PKU patients receiving a mixture of LNAA establishes a limited retention of nitrogen. Whether lysine could be the limiting amino acid remains to be determined by new short-term N-balance studies, with lysine added to the LNAA mixture. Therefore, special caution should be taken in the long-term use in PKU patients of LNAA without any added lysine.

DOI: 10.1007/BF00711746

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@article{Dotremont1995NutritionalVO, title={Nutritional value of essential amino acids in the treatment of adults with phenylketonuria}, author={H. Dotremont and Baudouin François and M. Diels and Pete Gillis}, journal={Journal of Inherited Metabolic Disease}, year={1995}, volume={18}, pages={127-130} }