Normal and defective neuronal membranes: Structure and function

@article{Powers2001NormalAD,
  title={Normal and defective neuronal membranes: Structure and function},
  author={James M. Powers},
  journal={Journal of Molecular Neuroscience},
  year={2001},
  volume={16},
  pages={285-287}
}
Neuronal involvement in the peroxisomal disorders is divided into two main groups: developmental and postdevelopmental or degenerative. In the former the major lesions are neuronal migration abnormalities, which vary from severe in the cerebro-hepato-renal (Zellweger) syndrome (ZS) to mild in neonatal adrenoleukodystrophy. More common, but much less severe, are defects in neuronal differentiation or terminal migration, particularly involving the inferior medullary olives. Ultrastructural and… CONTINUE READING

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