Neuromuscular involvement in various types of Ehlers–Danlos syndrome

@article{Voermans2009NeuromuscularII,
  title={Neuromuscular involvement in various types of Ehlers–Danlos syndrome},
  author={Nicol C. Voermans and Nens van Alfen and Sigrid Pillen and Martin M Y Lammens and Joost Schalkwijk and Machiel Zwarts and Iris A.L.M. van Rooij and Ben C J Hamel and Baziel G.M. van Engelen},
  journal={Annals of Neurology},
  year={2009},
  volume={65}
}
Ehlers–Danlos syndrome (EDS) is a clinically and genetically heterogeneous group of heritable connective tissue disorders characterized by joint hypermobility, skin hyperextensibility, and tissue fragility. Muscle involvement is plausible based on recently discovered interactions between muscle cells and extracellular matrix molecules; however, muscle symptoms are only sporadically reported. We designed a cross‐sectional study to find out whether neuromuscular features are part of EDS. 
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