Neurological and spinal manifestations of the Ehlers–Danlos syndromes

@article{Henderson2017NeurologicalAS,
  title={Neurological and spinal manifestations of the Ehlers–Danlos syndromes},
  author={Fraser C. Henderson and Claudiu Austin and Edward C. Benzel and Paolo A. Bolognese and Richard G. Ellenbogen and Clair A Francomano and Candace Ireton and Petra M Klinge and Myles Koby and Donlin M. Long and Sunil Patel and Eric L. Singman and Nicol C. Voermans},
  journal={American Journal of Medical Genetics Part C: Seminars in Medical Genetics},
  year={2017},
  volume={175},
  pages={195 - 211}
}
The Ehlers–Danlos syndromes (EDS) are a heterogeneous group of heritable connective tissue disorders characterized by joint hypermobility, skin extensibility, and tissue fragility. This communication briefly reports upon the neurological manifestations that arise including the weakness of the ligaments of the craniocervical junction and spine, early disc degeneration, and the weakness of the epineurium and perineurium surrounding peripheral nerves. Entrapment, deformation, and biophysical… 

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