NK-Cell Enteropathy and Similar Indolent Lymphoproliferative Disorders: A Case Series With Literature Review

@article{Xia2019NKCellEA,
  title={NK-Cell Enteropathy and Similar Indolent Lymphoproliferative Disorders: A Case Series With Literature Review},
  author={Daniel Xia and Elizabeth A. Morgan and David Berger and Geraldine S. Pinkus and Judith A. Ferry and Lawrence R. Zukerberg},
  journal={American Journal of Clinical Pathology},
  year={2019},
  volume={151},
  pages={75–85}
}
Objectives We report four new cases of natural killer-cell enteropathy (NKCE) and similar lymphoproliferative disorders (LPDs), as well as review the literature concerning indolent natural killer (NK)-cell LPDs of the gastrointestinal tract. Methods Pathologic and clinical data were obtained from institutional/referral records. Results Patient 1 (45-year-old man) had anemia; a small intestinal lesion was endoscopically biopsied. Patient 2 (65-year-old woman) had biliary colic, treated with… 
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This report reports a unique case where an indolent lymphoproliferative disorder with features that resemble NK-cell enteropathy is encountered for the first time outside the gastrointestinal tract, specifically in the female genitourinary tract.
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Diagnostic approach to T- and NK-cell lymphoproliferative disorders in the gastrointestinal tract.
TLDR
In Asia and South America, it is not uncommon to see involvement of the gastrointestinal tract by EBV-associated extranodal NK/T cell lymphoma, nasal type, which must be distinguished from NK cell enteropathy and EBv-associated mucocutaneous ulcers.
Overview of Gastrointestinal Lymphoproliferative disorders✰.
TLDR
An overview of WHO classification of digestive tumors and World Health Organization (WHO) classification of tumors of hematopoietic and lymphoid tissue is discussed focusing on the changes in the most recent WHO texts.
Genetic and phenotypic characterization of indolent T-cell lymphoproliferative disorders of the gastrointestinal tract
TLDR
Targeted next-generation sequencing and comprehensive immunophenotypic analysis of indolent T-cell lymphoproliferative disorders of the gastrointestinal tract provides insights into the pathogenetic bases of these diseases and confirms the heterogeneous nature ofThese diseases.
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This report reports a unique case where an indolent lymphoproliferative disorder with features that resemble NK-cell enteropathy is encountered for the first time outside the gastrointestinal tract, specifically in the female genitourinary tract.
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