Myelinoclastic diffuse sclerosis (Schilder's disease): report of a case and review of the literature

@article{Kotil2002MyelinoclasticDS,
  title={Myelinoclastic diffuse sclerosis (Schilder's disease): report of a case and review of the literature},
  author={Kadir Kotil and Murat Kalaycı and Tankut K{\"o}seoḡlu and Armağan Tuğrul},
  journal={British Journal of Neurosurgery},
  year={2002},
  volume={16},
  pages={516 - 519}
}
Schilder's myelinoclastic diffuse sclerosis is a rare demyelinating disease, which often mimics intracranial neoplasm or abscess. This disease is of importance to the neurosurgeon in that the clinical manifestations and course may closely simulate brain tumour, including the development of papilloedema and other signs of increased intracranial pressure. We have treated a 29-year-old right-handed young man presenting with left hemiplegia, aphasia and behavioural changes. Magnetic resonance… 

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TLDR
Because of the rapid and dramatic fluctuations in the patient's functional status, it has been possible to obtain sequential CT and comparative MR scans that graph­ ically document the interplay of cavitary and diffuse white­ matter lesions, which has allowed cliniconeuroradiologic assessment of this rare but distinctive inflammatory myelino­ clastic condition.

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TLDR
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TLDR
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