Multicenter Experience With Catheter Ablation for Ventricular Tachycardia in Lamin A/C Cardiomyopathy

@article{Kumar2016MulticenterEW,
  title={Multicenter Experience With Catheter Ablation for Ventricular Tachycardia in Lamin A/C Cardiomyopathy},
  author={Saurabh Kumar and Alexander F.A. Androulakis and Jean Marc Sellal and Philippe Maury and Estelle Gandjbakhch and Xavier Waintraub and Anne Rollin and Pascale Richard and Philippe Charron and Samuel H. Baldinger and Ciorsti J Macintyre and Bruce Koplan and Roy M. John and Gregory F. Michaud and Katja Zeppenfeld and Fr{\'e}d{\'e}ric Sacher and Neal K. Lakdawala and William G. Stevenson and Usha B. Tedrow},
  journal={Circulation: Arrhythmia and Electrophysiology},
  year={2016},
  volume={9},
  pages={e004357}
}
Background— Lamin A/C (LMNA) cardiomyopathy is a genetic disease with a proclivity for ventricular arrhythmias. We describe the multicenter experience with percutaneous catheter ablation of sustained monomorphic ventricular tachycardia (VT) in LMNA cardiomyopathy. Methods and Results— Twenty-five consecutive LMNA mutation patients from 4 centers were included (mean age, 55±9 years; ejection fraction, 34±12%; VT storm in 36%). Complete atrioventricular block was present in 11 patients; 3… 

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