Moyamoya disease and moyamoya syndrome.

@article{Scott2009MoyamoyaDA,
  title={Moyamoya disease and moyamoya syndrome.},
  author={R. Michael Scott and Edward R. Smith},
  journal={The New England journal of medicine},
  year={2009},
  volume={360 12},
  pages={
          1226-37
        }
}
Moyamoya disease is a cerebrovascular condition predisposing affected patients to stroke in association with progressive stenosis of the intracranial internal carotid arteries and their proximal branches. Patients with characteristic moyamoya vasculopathy plus associated conditions are categorized as having moyamoya syndrome. This review describes the demographic characteristics, pathogenesis, evaluation, and treatment of moyamoya disease and syndrome. 
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