Moyamoya disease and moyamoya syndrome.
@article{Scott2009MoyamoyaDA, title={Moyamoya disease and moyamoya syndrome.}, author={R. Michael Scott and Edward R. Smith}, journal={The New England journal of medicine}, year={2009}, volume={360 12}, pages={ 1226-37 } }
Moyamoya disease is a cerebrovascular condition predisposing affected patients to stroke in association with progressive stenosis of the intracranial internal carotid arteries and their proximal branches. Patients with characteristic moyamoya vasculopathy plus associated conditions are categorized as having moyamoya syndrome. This review describes the demographic characteristics, pathogenesis, evaluation, and treatment of moyamoya disease and syndrome.
1,166 Citations
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References
SHOWING 1-10 OF 118 REFERENCES
Surgical management of moyamoya syndrome.
- MedicineSkull base : official journal of North American Skull Base Society ... [et al.]
- 2005
The use of pial synangiosis is a safe, effective, and durable method of cerebral revascularization in moyamoya syndrome and should be considered as a primary treatment for moysamoya, especially in the pediatric population.
Surgical treatment of moyamoya disease in pediatric age.
- MedicineJournal of neurosurgical sciences
- 2001
C cerebral revascularization (by means of a simple operation like the EMS) in children with moyamoya disease is worthwhile, provided that the operation be performed before irreversible cerebral damage is established; however, even under these circumstances the operation can at least stop the progression of the disease.
Moyamoya disease‐‐a review.
- MedicineStroke
- 1983
Treatment with perivascular sympathectomy and superior cervical ganglionectomy may be useful but more investigation needs to be carried out into the pathogenesis of the disease before more definitive therapy is realized.
Recent experience with Moyamoya disease in Turkey
- MedicineEuropean Radiology
- 2000
Moyamoya, a rare but potentially devastating disease, must be addressed as a cause of haemorrhagic and ischaemic cerebral events.
Cerebrovascular occlusive disease with and without the moyamoya vascular network in children.
- Medicine, PsychologyNeuropediatrics
- 1985
Preipitating factors for ischemic attacks included deep breathing, changes in body temperature or sleep-waking transition were present in both groups and Etiology in some children was considered to be congenital.
Histological features of middle cerebral arteries from patients treated for Moyamoya disease.
- MedicineNeurologia medico-chirurgica
- 2007
Histological examination showed that MCA specimens from patients with MMD had significantly thinner media and thicker intima than control specimens and abnormal findings of the internal elastic lamina and eosin-positive deposits in the intima were detected.
Progression of disease in unilateral moyamoya syndrome.
- MedicineNeurosurgical focus
- 2008
Several factors, including contralateral abnormalities on initial imaging, congenital cardiac anomaly, previous cranial irradiation, Asian ancestry, and familial moyamoya syndrome, were associated with an increased risk of progression.
Cerebrovascular abnormalities in a population of children with neurofibromatosis type 1
- MedicineNeurology
- 2005
Of 316 patients with NF1 who underwent brain MRI, 8 (2.5%) children were reported to have an abnormality of the cerebrovascular system, including narrowed or ectatic vessels, vascular stenoses, aneurysm, and moyamoya.
Cerebral revascularization for moyamoya disease in children.
- MedicineNeurosurgery clinics of North America
- 2001
Moyamoya Syndrome Associated With Down Syndrome: Outcome After Surgical Revascularization
- MedicinePediatrics
- 2005
The clinical, radiologic, and angiographic features of moyamoya syndrome associated with Down syndrome seem comparable to those of primary moyAMoya disease, and Cerebral revascularization surgery with the pial synangiosis technique seems to confer long-lasting protection against additional strokes in this patient population.