Malignant pigmented clear cell epithelioid cell tumor (PEComa) in an adolescent boy with widespread metastases: a rare entity in this age group

Abstract

Malignant pigmented clear cell epithelioid cell tumor of the kidney is a rare variant of perivascular epithelioid cells tumors (PEComa) or epithelioid angiomyolipoma (AML). PEComa is characteristically composed purely of epitheloid cells. The fat cells and the blood vessels that are typical of classic AML are absent. Most epithelioid AML cases are benign… (More)
DOI: 10.1007/s00247-011-2125-0

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Cite this paper

@article{Rasalkar2011MalignantPC, title={Malignant pigmented clear cell epithelioid cell tumor (PEComa) in an adolescent boy with widespread metastases: a rare entity in this age group}, author={Darshana Dattatray Rasalkar and Winnie Chiu-wing Chu and Anthony W. H. Chan and Frankie Wai Tsoi Cheng and Chi K Li}, journal={Pediatric Radiology}, year={2011}, volume={41}, pages={1587-1590} }