Clinical features of morning glory syndrome were studied in 8 eyes of 7 patients. The cases were divided into two groups according to the size of the elevated peripapillary white ring. The size of the ring was expressed as an average disk diameter of normal control eyes. In 2 eyes of Group I with the ring less than 2.0 disk diameters, white tissue on the disk was less pronounced than in Group II, and vascular pattern in the posterior retina was almost normal. The macular ring reflex was present. In 6 eyes of Group II with the ring exceeding 2.0 disk diameters, white tissue on the disk was more marked than in Group I, and retinal vessels were narrow and extended straight toward the midperiphery. the macula was not formed, but a yellowish retinal area was observed on the center or temporal part of the elevated peripapillary white ring. It was concluded that in morning glory syndrome the macula may often by involved when anomaly of the optic disk is remarkable.