Long-term outcome after partial external biliary diversion for progressive familial intrahepatic cholestasis.

@article{Halaweish2010LongtermOA,
  title={Long-term outcome after partial external biliary diversion for progressive familial intrahepatic cholestasis.},
  author={Ihab F. Halaweish and Walter J. Chwals},
  journal={Journal of pediatric surgery},
  year={2010},
  volume={45 5},
  pages={934-7}
}
BACKGROUND Though patients with progressive familial intrahepatic cholestasis (PFIC) typically require liver transplantation, initial surgical treatment includes partial biliary diversion (PBD) to relieve jaundice-associated pruritus. This study was undertaken to describe long-term PFIC outcome data, which are currently sparsely reported. METHODS Retrospective review of 7 patients diagnosed with PFIC who underwent PBD between 2004 and 2008 was directed toward long-term postoperative outcome… CONTINUE READING