Long-term follow-up of MRI changes in thigh muscles of patients with Facioscapulohumeral dystrophy: A quantitative study

  title={Long-term follow-up of MRI changes in thigh muscles of patients with Facioscapulohumeral dystrophy: A quantitative study},
  author={Farzad Fatehi and Emmanuelle Salort-Campana and Arnaud Le Troter and {\'E}milie Lareau-Trudel and Mark Bydder and Alexandre Four{\'e} and Maxime Guye and David Bendahan and Shahram Attarian},
  journal={PLoS ONE},
Facioscapulohumeral muscular dystrophy (FSHD) is one of the most common hereditary muscular disorders. Currently FSHD has no known effective treatment and detailed data on the natural history are lacking. Determination of the efficacy of a given therapeutic approach might be difficult in FSHD given the slow and highly variable disease progression. Magnetic resonance imaging (MRI) has been widely used to qualitatively and quantitatively evaluate in vivo the muscle alterations in various… 

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