Long-term Outcomes of Pediatric-Onset Hypertrophic Cardiomyopathy and Age-Specific Risk Factors for Lethal Arrhythmic Events

  title={Long-term Outcomes of Pediatric-Onset Hypertrophic Cardiomyopathy and Age-Specific Risk Factors for Lethal Arrhythmic Events},
  author={N. Maurizi and S. Passantino and Gaia Spaziani and F. Girolami and A. Arretini and M. Targetti and I. Pollini and A. Tomberli and S. Pradella and G. Calabri and Veronica Vinattieri and B. Bertaccini and O. Leone and L. De Simone and C. Rapezzi and N. Marchionni and F. Cecchi and S. Favilli and I. Olivotto},
  journal={JAMA Cardiology},
  • N. Maurizi, S. Passantino, +16 authors I. Olivotto
  • Published 2018
  • Medicine
  • JAMA Cardiology
  • Importance Predictors of lethal arrhythmic events (LAEs) after a pediatric diagnosis of hypertrophic cardiomyopathy (HCM) are unresolved. Existing algorithms for risk stratification are limited to patients older than 16 years because of a lack of data on younger individuals. Objective To describe the long-term outcome of pediatric-onset HCM and identify age-specific arrhythmic risk factors. Design, Setting, and Participants This study assessed patients with pediatric-onset hypertrophic… CONTINUE READING
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