Living a Normal Life With the Nondominant Hemisphere: Magnetic Resonance Imaging Findings and Clinical Outcome for a Patient With Left-Hemispheric Hydranencephaly

@article{Ulmer2005LivingAN,
  title={Living a Normal Life With the Nondominant Hemisphere: Magnetic Resonance Imaging Findings and Clinical Outcome for a Patient With Left-Hemispheric Hydranencephaly},
  author={Stephan Ulmer and Friederike Moeller and Marc A. Brockmann and Johann P. Kuhtz-Buschbeck and Ulrich Stephani and Olav Jansen},
  journal={Pediatrics},
  year={2005},
  volume={116},
  pages={242 - 245}
}
In hemihydranencephaly, the human brain lacks 1 complete hemisphere. An occlusion of the carotid artery, affecting all supplied territories, is thought to be the underlying mechanism. This extremely rare disorder, of which only 7 cases have been reported to date, is thought to occur before the last trimester of gestation (20th to 27th week), after neural migration but before synaptogenesis. We report on a 36-year-old man born at term, with no complications, from nonconsanguineous healthy… 

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Discrepancy Between Cerebral Structure and Cognitive Functioning: A Review
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This article provides a review of noteworthy aspects of hydrocephalus, hemihydranencephaly, hemispherectomy, and certain abilities of “savants” and adds considerations on memory processing, comment on the assumed role of neural plasticity in these contexts, and highlight the importance of taking such anomalies into account when formulating encompassing models of brain functioning.
Left-Hemispheric Hydranencephaly With Less Favorable Findings: In Reply
TLDR
It is expected that 8 of 9 reported cases of hemihydranencephaly involve absent left hemispheres, which possibly may represent a difficulty in development when lacking the right hemisphere or a relative proclivity for lesion to the left hemisphere during development.
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