Liver transplantation for hereditary tyrosinemia in the presence of hepatocellular carcinoma.


H· EREDITARY TYROSINEMIA is a metabolic disorder characterized by deficiency of the enzyme fummarylacetoacetate, resulting in the accumulation of tyrosine metabolites, which are toxic to the liver. Hepatic dysfunction, associated with tyrosinemia, varies from an acute form of liver failure to a chronic, progressive form that leads to cirrhosis and… (More)

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