Liver Disease in Cystic Fibrosis

  title={Liver Disease in Cystic Fibrosis},
  author={C. Colombo and M. Russo and L. Zazzeron and G. Romano},
  journal={Journal of Pediatric Gastroenterology and Nutrition},
  • C. Colombo, M. Russo, +1 author G. Romano
  • Published 2006
  • Medicine
  • Journal of Pediatric Gastroenterology and Nutrition
  • Liver involvement in Cystic Fibrosis (CF) is much less frequent than both pulmonary and pancreatic diseases that are present in 80-90% of CF patients; liver disease (LD) affects only one third of CF patients, however, because of the decreasing mortality from extrahepatic causes, its recognition and management is becoming a relevant clinical issue. Recent observations suggest that clinical expression of LD in CF may be influenced by genetic modifiers; their identification is an important issue… CONTINUE READING
    45 Citations
    Cystic fibrosis-associated liver disease.
    • 70
    Hepatic Manifestations of Cystic Fibrosis.
    • 7
    Unexpected diagnosis of cystic fibrosis at liver biopsy: a report of four pediatric cases
    • 8
    Cirrhosis associated with decreased survival and a 10-year lower median age at death of cystic fibrosis patients in the Netherlands.
    • 9
    • PDF
    TIMP-1/-2 and transient elastography allow non invasive diagnosis of cystic fibrosis associated liver disease.
    • T. Rath, K. Menendez, +7 authors M. Roderfeld
    • Medicine
    • Digestive and liver disease : official journal of the Italian Society of Gastroenterology and the Italian Association for the Study of the Liver
    • 2012
    • 21
    The cystic fibrosis intestine.
    • 101
    • PDF
    EASL Clinical Practice Guidelines: Autoimmune hepatitis.
    • 452


    Epidemiology of liver disease in cystic fibrosis: a longitudinal study.
    • 145
    Liver cirrhosis in cystic fibrosis--therapeutic implications and long term follow up.
    • 123
    • PDF
    Liver manifestations of cystic fibrosis.
    • 35
    Natural history of liver disease in cystic fibrosis
    • 250
    • Highly Influential
    Epidemiology of cystic fibrosis-related diabetes.
    • 196
    Hepatocellular carcinoma in association with cirrhosis in a patient with cystic fibrosis.
    • 23
    Liver disease in cystic fibrosis: A prospective study on incidence, risk factors, and outcome
    • 259
    Analysis of risk factors for the development of liver disease associated with cystic fibrosis.
    • 159