Liver Disease in Cystic Fibrosis
@article{Colombo2006LiverDI, title={Liver Disease in Cystic Fibrosis}, author={C. Colombo and M. Russo and L. Zazzeron and G. Romano}, journal={Journal of Pediatric Gastroenterology and Nutrition}, year={2006}, volume={43}, pages={S49-S55} }
Liver involvement in Cystic Fibrosis (CF) is much less frequent than both pulmonary and pancreatic diseases that are present in 80-90% of CF patients; liver disease (LD) affects only one third of CF patients, however, because of the decreasing mortality from extrahepatic causes, its recognition and management is becoming a relevant clinical issue. Recent observations suggest that clinical expression of LD in CF may be influenced by genetic modifiers; their identification is an important issue… CONTINUE READING
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