Liver Disease in Cystic Fibrosis

@article{Colombo2006LiverDI,
  title={Liver Disease in Cystic Fibrosis},
  author={Carla Colombo and Maria Chiara Russo and Laura Zazzeron and Giovanna Romano},
  journal={Journal of Pediatric Gastroenterology and Nutrition},
  year={2006},
  volume={43},
  pages={S49-S55}
}
Liver involvement in Cystic Fibrosis (CF) is much less frequent than both pulmonary and pancreatic diseases that are present in 80-90% of CF patients; liver disease (LD) affects only one third of CF patients, however, because of the decreasing mortality from extrahepatic causes, its recognition and management is becoming a relevant clinical issue. Recent observations suggest that clinical expression of LD in CF may be influenced by genetic modifiers; their identification is an important issue… 
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