Keratoma hereditaria mutilans (Vohwinkel's disease) with congenital alopecia universalis (atrichia congenita).

@article{Bhatia1989KeratomaHM,
  title={Keratoma hereditaria mutilans (Vohwinkel's disease) with congenital alopecia universalis (atrichia congenita).},
  author={Krishan Kumar Bhatia and Sanjay R Chaudhary and Ujjal S Pahwa and G C Mehrotra},
  journal={The Journal of dermatology},
  year={1989},
  volume={16 3},
  pages={231-6}
}
A family is described in which a boy and two girls had features of keratoma hereditaria mutilans (Vohwinkel's disease) and congenital absence of hair. None of them had any hair at birth or developed any subsequently. They had congenital, nonscarring alopecia universalis. The skin over the palms and soles showed progressive thickening, which led to mutilating deformities of the hands and fingers. Histopathological examination of the scalp skin revealed no changes in the epidermis or dermis with… CONTINUE READING