Kaposiform Hemangioendothelioma: A Study of 33 Cases Emphasizing Its Pathologic, Immunophenotypic, and Biologic Uniqueness From Juvenile Hemangioma

@article{Lyons2004KaposiformHA,
  title={Kaposiform Hemangioendothelioma: A Study of 33 Cases Emphasizing Its Pathologic, Immunophenotypic, and Biologic Uniqueness From Juvenile Hemangioma},
  author={Lisa L Lyons and Paula E. North and Fernand Mac-Moune Lai and Mark H. Stoler and Andrew L. Folpe and Sharon Whelan Weiss},
  journal={The American Journal of Surgical Pathology},
  year={2004},
  volume={28},
  pages={559-568}
}
Kaposiform hemangioendothelioma (KH) is a rare tumor of childhood often associated with Kasabach-Merritt phenomenon (KMP) and occasionally lymphangiomatosis. Although generally considered distinct from other vascular neoplasms, its rarity has precluded a thorough study of its immunophenotypic profile and long-term behavior. Thirty-three cases of KH were reviewed and immunostained for alpha-smooth muscle actin, various endothelial markers (CD31, CD34, vWf, FLI1), a platelet marker (CD61), and… 

Kaposiform Hemangioendothelioma: clinicopathological characteristics of 8 cases of a rare vascular tumor and review of literature

TLDR
The clinicopathological features of 8 cases of KHE are described which will be helpful in making their diagnosis and knowledge about histological features and potential mimics is helpful in avoiding misdiagnosis.

Original Article Clinicopathological features of Kaposiform hemangioendothelioma

TLDR
The results suggest that KHE can occur in the embryonic period, and patients with KMP often have earlier onset time and larger lesional size.

Clinicopathological features of Kaposiform hemangioendothelioma.

TLDR
The results suggest that KHE can occur in the embryonic period, and patients with KMP often have earlier onset time and larger lesional size.

Adult-Onset Kaposiform Hemangioendothelioma in a Posttraumatic Site

TLDR
A rare patient is presented with adult-onset KHE arising in a posttraumatic location and treatment consists of drug therapy with corticosteroid, interferon, or vincristine.

Kaposiform hemangioendothelioma with distant lymphangiomatosis without an association to Kasabach-Merritt-Syndrome in a female adult!

TLDR
The association of KHE in a female adult with lymphangioma rather than KMS in this case supports the hypothesis that such an association may represent a benign subform of this disease in an adult and excision seems to be curative.

Intracranial kaposiform hemangioendothelioma: proposal of a new malignant variant.

TLDR
A case of a KHE without Kasabach-Merritt syndrome arising from the right tentorium cerebelli in a 13-month-old male child is reported, which may be not only the first intracranial extraaxial KHE, but also the first truly malignant variant.

Kaposiform hemangioendothelioma/Kasabach–Merritt syndrome. Сlinical and laboratory characteristics. Analysis of clinical cases

TLDR
Despite the presence of clear clinical and laboratory characteristics of KMS, some cases require differential diagnosis with other vascular anomalies accompanied by thrombocytopenia and consumption coagulopathy – with congenital hemangiomas (rapidly involuting congenitalhemangioma), multifocal lymphangioendotheliomatosis, kaposiform lymphangiom atosis, venous malformations.

Kaposiform hemangioendothelioma in tonsil of a child associated with cervical lymphangioma: a rare case report

TLDR
This case forms the second documented case of KHE occurring in tonsil of a child, associated with a neck swelling, but unassociated with KMP, along with its unique association with neck lymphangioma.
...

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TLDR
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TLDR
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TLDR
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TLDR
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TLDR
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TLDR
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TLDR
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TLDR
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