Infant Case with a Malignant Form of Brugada Syndrome

@article{Suzuki2000InfantCW,
  title={Infant Case with a Malignant Form of Brugada Syndrome},
  author={H. Suzuki and Katsumi Torigoe and Osamu Numata and S. Yazaki},
  journal={Journal of Cardiovascular Electrophysiology},
  year={2000},
  volume={11}
}
Infant with Brugada Syndrome. We report a 6‐nionth‐old Japanese infant with a malignant form of Brugada syndrome, who had frequent episodes of ventricular fibriitation (VF) and nonsustained polymorphic ventricular tachycardia (VT). To the best of our knowledge, this infant is the youngest patient reported to have Brugada syndrome. Continuous infusion of a β‐adrenergic agonist and intravenous injection of a parasympathetic antagonist suppressed the electrical storm of polymorphic VT and VF… Expand
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TLDR
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TLDR
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TLDR
Brugada syndrome has been the subject of a number of controversies with regard to its pathophysiology; the prognosis of asymptomatic individuals and the best way to establish their risk; and the causal role of genetic variants, including the role of sodium channel mutations. Expand
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