Improving life expectancy of patients with scleroderma: results from the South Australian Scleroderma Register

@article{Kennedy2018ImprovingLE,
  title={Improving life expectancy of patients with scleroderma: results from the South Australian Scleroderma Register},
  author={Nicholas Kennedy and Jenny G Walker and Paul Hakendorf and Peter Roberts-Thomson},
  journal={Internal Medicine Journal},
  year={2018},
  volume={48}
}
BACKGROUND Scleroderma is a rare connective tissue disorder characterised by inflammation, vasculopathy and excessive fibrosis. [] Key MethodMETHODS Utilising the South Australian Scleroderma Register, deceased patients were identified. We examined changes in age of death and duration of disease in these patients over three time periods: 1985-1994, 1995-2004 and 2005-2015. Analyses of scleroderma subtypes were performed, and comparisons were made to the general South Australian population.

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