IgG4-Related Disease Causing Rapid Evolution of a Severe Aortic Valvular Stenosis.

Abstract

Immunoglobulin G4-related systemic disease (IgG4-RSD) is a recognized emerging entity characterized by chronic fibroinflammation that can affect every organ but rarely affects the cardiovascular system. We report a rare case of IgG4-RSD involving an aortic valve that resulted in rapid progression of an aortic valvular stenosis and was successfully treated by aortic valve replacement and corticosteroids.

DOI: 10.1016/j.athoracsur.2016.08.045

Cite this paper

@article{Bruls2017IgG4RelatedDC, title={IgG4-Related Disease Causing Rapid Evolution of a Severe Aortic Valvular Stenosis.}, author={Samuel Bruls and Audrey Courtois and Philippe Delvenne and Roland Hustinx and Michel P. Moutschen and Laurence de Leval and Jean-Olivier Defraigne and Natzi Sakalihasan}, journal={The Annals of thoracic surgery}, year={2017}, volume={103 3}, pages={e239-e240} }