IgA-epidermolysis bullosa acquisita in a child resulting in blindness.

@article{Caux1997IgAepidermolysisBA,
  title={IgA-epidermolysis bullosa acquisita in a child resulting in blindness.},
  author={Fr{\'e}d{\'e}ric Caux and Gudula Kirtschig and Françoise Lemarchand-Venencie and Pierre Y. Venencie and Thanh Hoang-Xuan and H. Robin and Louis Dubertret and Catherine Prost},
  journal={The British journal of dermatology},
  year={1997},
  volume={137 2},
  pages={
          270-5
        }
}
Epidermolysis bullosa acquisita (EBA) is an acquired subepidermal bullous disease characterized by IgG autoantibodies directed against type VII collagen, the major component of anchoring fibrils. The classical phenotype of EBA is a non-inflammatory, mechanobullous disease resembling the dystrophic forms of inherited epidermolysis bullosa. Mucous membrane involvement is frequent but usually mild. We report a 1-year-old girl suffering from IgA-EBA, who presented with an initial eruption of… CONTINUE READING

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