Idiopathic pulmonary arterial hypertension and pulmonary veno-occlusive disease: similarities and differences.

  title={Idiopathic pulmonary arterial hypertension and pulmonary veno-occlusive disease: similarities and differences.},
  author={David Montani and Kristina Kemp and Peter Dorfmuller and Olivier Sitbon and G{\'e}rald Simonneau and Marc Humbert},
  journal={Seminars in respiratory and critical care medicine},
  volume={30 4},
Pulmonary veno-occlusive disease (PVOD) is a rare disorder and can be misdiagnosed as idiopathic pulmonary arterial hypertension (iPAH). PVOD and iPAH often share a similar clinical presentation, genetic background, and hemodynamic profile. PVOD accounts for 5 to 10% of cases initially considered as iPAH. When compared with iPAH, PVOD is characterized by a higher male:female ratio, higher tobacco exposure, and lower PaO (2) at rest, diffusing capacity for carbon monoxide (DLCO), and oxygen… CONTINUE READING


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