Idiopathic Short QT Interval:A New Clinical Syndrome?

  title={Idiopathic Short QT Interval:A New Clinical Syndrome?},
  author={Ihor Gussak and Pedro Brugada and Josep Brugada and R. Scott Wright and Stephen L. Kopecky and Bernard R. Chaitman and Preben Bjerregaard},
  pages={99 - 102}
In this first clinical report of an idiopathic familial persistently short QT interval (QTI), we describe three members of one family (a 17-year-old female, her 21-year-old brother, and their 51-year-old mother) demonstrating this ECG phenomenon, associated in the 17-year-old with several episodes of paroxysmal atrial fibrillation requiring electrical cardioversion. Similar ECG changes seen in an unrelated 37-year-old patient were associated with sudden cardiac death. Our report also describes… 

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