Idiopathic Short QT Interval:A New Clinical Syndrome?

@article{Gussak2000IdiopathicSQ,
  title={Idiopathic Short QT Interval:A New Clinical Syndrome?},
  author={I. Gussak and P. Brugada and J. Brugada and R. Wright and S. Kopecky and B. Chaitman and P. Bjerregaard},
  journal={Cardiology},
  year={2000},
  volume={94},
  pages={99 - 102}
}
In this first clinical report of an idiopathic familial persistently short QT interval (QTI), we describe three members of one family (a 17-year-old female, her 21-year-old brother, and their 51-year-old mother) demonstrating this ECG phenomenon, associated in the 17-year-old with several episodes of paroxysmal atrial fibrillation requiring electrical cardioversion. Similar ECG changes seen in an unrelated 37-year-old patient were associated with sudden cardiac death. Our report also describes… Expand
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