Hypoplastic pulmonary arteries and aorta with obstructive uropathy in 2 siblings.

@article{Kashani1984HypoplasticPA,
  title={Hypoplastic pulmonary arteries and aorta with obstructive uropathy in 2 siblings.},
  author={Iraj A. Kashani and Charles M. Strom and J E Utley and Jos{\'e} Mar{\'i}n-Garc{\'i}a and Charles Higgins},
  journal={Angiology},
  year={1984},
  volume={35 4},
  pages={252-6}
}
Two sisters who presented with diffuse hypoplasia of pulmonary arteries, relative hypoplasia of ascending aorta, obstructive uropathy, bilateral ureteral reflux, and hydronephrosis, are described. The subsequent course was characterized by progressive and gradual onset of right heart failure, failure to thrive, chronic malabsorption and systemic… CONTINUE READING