Hypocomplementemic autosomal recessive hemolytic uremic syndrome with decreased factor H

@article{Ohali1998HypocomplementemicAR,
  title={Hypocomplementemic autosomal recessive hemolytic uremic syndrome with decreased factor H},
  author={Melly Ohali and Hanna Shalev and Menachem Schlesinger and Yitzhak Katz and Leonid Kachko and Rivka Carmi and Shaul Sofer and Daniel Landau},
  journal={Pediatric Nephrology},
  year={1998},
  volume={12},
  pages={619-624}
}
We describe the clinical course, complement components, and pathological findings of 10 infants with autosomal recessive hemolytic uremic syndrome (HUS). All patients were members of one extended highly inbred Bedouin kindred. The median age of presentation was 2 weeks (range 1–20 weeks). Eight patients died, 2 patients are alive, on dialysis. Renal biopsies revealed thrombotic microangiopathy with a predominant early arteriolar involvement and subsequent development of ischemic glomerular… CONTINUE READING

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Antiendothelial cell antibodies (AECA) correlate with the activities of lupus (abstract)

  • Y Ikeda, T Fujimoto, +4 authors K Dohi
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