History, anatomic forms, and pathogenesis of Chiari I malformations

@article{Schijman2003HistoryAF,
  title={History, anatomic forms, and pathogenesis of Chiari I malformations},
  author={Edgardo Schijman},
  journal={Child's Nervous System},
  year={2003},
  volume={20},
  pages={323-328}
}
  • E. Schijman
  • Published 5 February 2004
  • Medicine
  • Child's Nervous System
IntroductionChiari I malformations constitute a group of entities of congenital or acquired etiology that have in common descent of the cerebellar tonsils into the cervical spinal canal. In recent years, since the advent of magnetic resonance imaging, an increasing number of asymptomatic, doubtfully symptomatic, and minimally symptomatic patients with Chiari I malformations have been diagnosed. This has resulted in controversy about the multiple therapeutic strategies indicated for these… 
Current Concepts in the Pathogenesis, Diagnosis, and Management of Type I Chiari Malformations.
TLDR
Type 1 Chiari malformations are a group of congenital or acquired disorders which include the abnormal presence of the cerebellar tonsils in the upper spinal canal, rather than the posterior fossa, which causes crowding of the structures at the craniocervical junction.
CHIARI MALFORMATION TYPE I – CASE REPORT AND REVIEW OF LITERATURE
TLDR
The case of a 44 year old woman with Chiari type I malformation and associated cervical syringomyelia is reported.
Chiari type I malformation in children.
TLDR
This paper reports on the state of the art and the recent achievements about CIM aiming at providing further information especially on the pathogenesis, the natural history, and the management of the malformation, which are the most controversial aspects.
Benign Chiari I Malformation
TLDR
A benign Chiari I malformation is one with minimal or no classical symptoms at presentation and no imaging evidence of syringomyelia, hydrocephalus, or spinal cord signal change and it is recommended clinical and radiographic follow-up of patients with benign CM I.
Surgical Management of Patients with Chiari I Malformation
TLDR
A systematic and critical review of the pertinent literature was made for identifying the most commonly employed surgical procedures in the management of patients with symptomatic CM-I.
The pediatric Chiari I malformation: a review
TLDR
Analyzes the literature regarding this form of hindbrain herniation in regard to definition, anatomy, pathobiology, symptoms, findings, treatment, and outcomes to elucidate the optimal selection and treatment criteria.
Primary Cerebellar Tuberculoma in Arnold-Chiari Malformation Mimicking Posterior Cranial Fossa Tumor: The First Report
TLDR
Brain magnetic resonance imaging confirmed a hypointense signal mass in the left hemisphere of the cerebellum causing mass effects on the fourth ventricle, which shifted it, accompanied with dilation of third and lateral ventricles.
Chiari Malformation and Syringomyelia
TLDR
Chiari malformations are a group of abnormalities of the hindbrain that were originally described in 1891 by Hans Chiari, a German professor, who created the classic definitions of hindbrain herniation now described as Chiari type I (CIM), ChiariType II (CIIM), and Chiaritype III (CIIIM) mal Formations.
Chiari Malformation and Syringomyelia
TLDR
This chapter discusses the pathophysiology, etiology, presenting symptoms, radiodiagnostic imaging, surgical management, and nursing care of children with Chiari malformation and/or syringomyelia.
Chiari malformations: An important cause of pediatric aspiration.
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