High-dose intravenous immunoglobulins dramatically reverse systemic capillary leak syndrome

@article{Lambert2008HighdoseII,
  title={High-dose intravenous immunoglobulins dramatically reverse systemic capillary leak syndrome},
  author={Marc Lambert and David Launay and Eric Hachulla and Sandrine Morell-Dubois and Vincent Soland and Viviane Queyrel and François Fourrier and Pierre-yves Hatron},
  journal={Critical Care Medicine},
  year={2008},
  volume={36},
  pages={2184-2187}
}
Objective:The objective of this study was to report the dramatic improvement of patients with systemic capillary leak syndrome obtained with high-dose intravenous immunoglobulins. Design:Systemic capillary leak syndrome is a rare and life-threatening disorder characterized by hypotension that can lead to shock, weight gain, hypoalbuminemia, and elevated hematocrit secondary to unexplained episodic capillary fluid extravasation into the interstitial space. Because its cause is unknown, systemic… 
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An up-to-date, evidence-based review of the understanding of Idiopathic systemic capillary leak syndrome and its management in the light of currently available evidence is provided.
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