Hereditary sensory and autonomic neuropathies

  title={Hereditary sensory and autonomic neuropathies
  author={Felicia B. Axelrod},
  journal={Clinical Autonomic Research},
  • F. Axelrod
  • Published 1 April 2002
  • Medicine
  • Clinical Autonomic Research
The hereditary sensory and autonomic neuropathies (HSAN) are a group of rare, clinically and genetically heterogeneous disorders. A numerical classification (type I to V) based on clinical phenotype and pattern of inheritance is widely used but additional entities have been described. With the exception of HSAN type I, which has a dominant pattern of inheritance, all other HSANs are autosomal recessive traits. Diagnosis of the HSANs depends on clinical examinations and detailed sensory and… 

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