Hereditary and acquired ichthyosis vulgaris

@article{Okulicz2003HereditaryAA,
  title={Hereditary and acquired ichthyosis vulgaris},
  author={Jason F. Okulicz and Robert A. Schwartz},
  journal={International Journal of Dermatology},
  year={2003},
  volume={42}
}

Topics from this paper

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Poster
1 Philipps-Universität Marburg, Dermatologie, Marburg, Deutschland 2 Ludwig-Maximilians-Universität, Klinik für Dermatologie und Allergologie, München, Deutschland 3 Universitätsklinikum Lübeck,
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A review on the pathophysiology of nonsyndromic ichthyosis as an epidermal genodermatosis
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Sight-threatening Complication of Cicatricial Ectropion in a Patient with Lamellar Ichthyosis - Case Report.
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A case of lamellar ichthyosis and sight-threatening complications of cicatricial ectropion in an adult male patient which was surgically managed with tectonic penetrating keratoplasty with no perioperative complications is reported.
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References

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Ultrastructural distinction of autosomal dominant ichthyosis vulgaris and X-linked recessive ichthyosis
SummaryIn autosomal dominant ichthyosis vularis ultrastructural studies have revealed a severe disturbance of keratohyalin synthesis by which this entity may clearly be distinguished from X-linked
Anaplastic large-cell lymphoma associated with acquired ichthyosis
TLDR
A 74-year-old Japanese man with ALCL, involving lymph nodes and the skin, who exhibited acquired ichthyosis is described, which is the second case report of acquired ICHthyosis associated withALCL.
Loss of normal profilaggrin and filaggrin in flaky tail (ft/ft) mice: an animal model for the filaggrin-deficient skin disease ichthyosis vulgaris.
TLDR
It is proposed that the absence of filag Grin, and in particular the hygroscopic, filaggrin-derived amino acids that are thought to function in epidermal hydration, underlies the dry, scaly skin characteristic of ft/ft mice.
Effect of topical tazarotene in the treatment of congenital ichthyoses
TLDR
Short‐term topical application of tazarotene 0.05% gel is a very effective and well‐tolerated treatment modality in different forms of congenital ichthyoses and may be an alternative to systemic retinoid therapy.
Reduced Stability and Bi-Allelic, Coequal Expression of Profilaggrin mRNA in Keratinocytes Cultured From Subjects With Ichthyosis Vulgaris
TLDR
Evidence is presented that profilaggrin mRNA in keratinocytes cultured from subjects with IV is intrinsically unstable and has a shorter half-life compared with that in normal cells, and a model in which a labile ribonuclease and a stabilizing factor may modulate the Profilag Grin mRNA steady-state level is suggested.
Dermatomyositis and acquired ichthyosis as paraneoplastic manifestations of ovarian tumor
TLDR
Treatment with prednisone, 1 mg/kg per day, was started, with improvement, in two cases of dermatomyositis in a 37‐year‐old white woman.
Acquired ichthyosis in bone marrow transplant recipients.
TLDR
AI is a previously unreported cutaneous complication of bone marrow transplantation that may be related to graft-versus-host disease in these patients and appears to be unrelated to specific drug therapy.
Decreased Profilaggrin Expression in Ichthyosis Vulgaris Is a Result of Selectively Impaired Posttranscriptional Control (*)
TLDR
The results indicate that defective profilaggrin expression in ichthyosis vulgaris is a result of selectively impaired posttranscriptional control.
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Acquired ichthyosis in concomitant HIV-1 and HTLV-II infection: a new association with intravenous drug abuse.
TLDR
Assessment of 184 male and female HIV-1-positive intravenous drug users for acquired ichthyosis found that it occurred only after profound helper T-cell depletion, in association with increasing age, and with concomitant infection with HTLV-II.
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