Hereditary Prosopagnosia: the First Case Series

@article{Grueter2007HereditaryPT,
  title={Hereditary Prosopagnosia: the First Case Series},
  author={Martina Grueter and Thomas Grueter and Vaughan Bell and J. Horst and Wolfgang Laskowski and Karl Sperling and Peter W. Halligan and Hadyn D. Elli and Ingo Kennerknecht},
  journal={Cortex},
  year={2007},
  volume={43},
  pages={734-749}
}

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References

SHOWING 1-10 OF 51 REFERENCES

A Fifteen Year Follow-Up of a Case of Developmental Prosopagnosia

Developmental prosopagnosia: A study of three patients

Severe Developmental Prosopagnosia in a Child With Superior Intellect

  • R. JonesD. Tranel
  • Psychology
    Journal of clinical and experimental neuropsychology
  • 2001
A novel finding was that the childs covert recognition of familiar faces based on an autonomic index was normal, suggesting that as in some adult-onset cases, the brain is capable of acquiring some information about familiar faces, even without conscious recognition.

Prosopagnosia and alexia without object agnosia.

Following a trauma causing bilateral posterior brain damage, a patient complained of dyslexia and prosopagnosia, but not object agnosia. On testing she showed intact recognition of object drawings,

Covert recognition in acquired and developmental prosopagnosia

Extensive right occipitotemporal lesions with significant deficits in face perception are not incompatible with covert face processing, indicating that these are related phenomena.

Childhood prosopagnosia

Detailed Exploration of Face-related Processing in Congenital Prosopagnosia: 1. Behavioral Findings

The findings elucidate the psychological mechanisms underlying congenital prosopagnosia and support the link between configural and face processing.

First report of prevalence of non‐syndromic hereditary prosopagnosia (HPA)

This study provides epidemiological evidence that congenital PA is a very common cognitive disorder which almost always runs in families and is fully compatible with autosomal dominant inheritance.

Disordered recognition of facial identity and emotions in three Asperger type autists

In all three boys these facial processing deficits were more or less isolated, and general visuospatial functions, attention, formal language and scholastic performances were normal or even highly developed with the exception of deficient gestalt perception in B.
...