Hepatoportal sclerosis in childhood.

  title={Hepatoportal sclerosis in childhood.},
  author={Jo{\~a}o Gilberto Maksoud and S{\'e}rgio Mies and L C da Costa Gayotto},
  journal={American journal of surgery},
  volume={151 4},
The clinical, angiographic, and pathologic features of hepatoportal sclerosis in five children are presented. Hepatosplenomegaly with preservation of liver function and esophageal varices were demonstrated. Histologically, portal alterations were consistent and prominent and included subintimal sclerosis of the intrahepatic venous branches and telangiectases. Angiographic patterns were variable, but all exhibited intrahepatic portal venous obstruction. In three patients, there was an… CONTINUE READING