Hepatic and renal manifestations in autosomal dominant polycystic kidney disease: a dichotomy of two ends of a spectrum.

@article{Gulick2011HepaticAR,
  title={Hepatic and renal manifestations in autosomal dominant polycystic kidney disease: a dichotomy of two ends of a spectrum.},
  author={J J M van Gulick and Tom J G Gevers and Loes van Keimpema and Joost P H Drenth},
  journal={The Netherlands journal of medicine},
  year={2011},
  volume={69 9},
  pages={
          367-71
        }
}
Autosomal dominant polycystic kidney disease (ADPKD) is a multisystem disorder. It is the most common genetic cause of end-stage renal disease. One frequent extra-renal manifestation is hepatic cyst formation. The majority of ADPKD patients develop complications as a result of renal cyst formation; however, a small proportion develop extensive hepatic disease with minor renal features. Both phenotypes seem to represent the spectrum of ADPKD. This review discusses the current understanding of… CONTINUE READING

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