Hemophagocytic syndrome as a complication in a patient with Sézary syndrome.


Hemophagocytic syndrome (HPS) is a rare disorder and is often fatal despite treatment. It is caused by a dysregulation in natural killer (NK)/T cell function, resulting in the activation and proliferation of lymphocytes or histiocytes with uncontrolled hemophagocytosis and cytokine overproduction. It can be either primary, with a genetic etiology, or… (More)
DOI: 10.1111/j.1365-4632.2011.05286.x


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