Granulomatosis with polyangiitis (Wegener's): An alternative name for Wegener's granulomatosis

@article{Falk2011GranulomatosisWP,
  title={Granulomatosis with polyangiitis (Wegener's): An alternative name for Wegener's granulomatosis},
  author={Ronald J. Falk and Wolfgang Ludwig Gross and Lo{\"i}c Guillevin and Gary S. Hoffman and David R. W. Jayne and John Charles Jennette and Cees G. M. Kallenberg and Raashid A Luqmani and Alfred Mahr and Eric L. Matteson and Peter A. Merkel and Ulrich Specks and Richard A. Watts},
  journal={Annals of the Rheumatic Diseases},
  year={2011},
  volume={70},
  pages={704 - 704}
}
The Boards of Directors of the American College of Rheumatology (ACR), American Society of Nephrology (ASN) and the European League Against Rheumatism (EULAR) have recommended a gradual shift from honorific eponyms to disease-descriptive or aetiology-based nomenclature. The leadership of these three organizations tasked an international group of senior academicians expert in the care of patients with vasculitis and engaged in research in the field to provide the medical community with proper… 
Granulomatosis with polyangiitis
From Churg-Strauss Syndrome to Eosinophilic Granulomatosis With Polyangiitis: A Historical Review of Nomenclature and Diagnostic Criteria.
TLDR
Key historical advances in the diagnosis, classification, and nomenclature of EGPA that have shaped the understanding of this protean disorder over time are reviewed.
Proposal for a more practical classification of antineutrophil cytoplasmic antibody-associated vasculitis
TLDR
The limitations of the currently used classification are discussed and an alternative, simple classification according to ANCA type and organ involvement is proposed, which provides important clinical information of prognosis and outcomes.
Hypertrophic pachymeningitis and orbital tumor associated with Granulomatosis with polyangiitis: report of a clinical case
A 65-year-old patient, with a diagnosis of Granulomatosis with Polyangeitis (GPA) of 18 years of evolution, whose debut was with respiratory failure and hemoptysis, receiving induction treatment with
The Many Faces of Granulomatosis With Polyangiitis: A Review of the Head and Neck Imaging Manifestations.
TLDR
Although there are no reliable pathognomonic imaging features for GPA, the present article attempts to identify patterns of disease that are suggestive of the disease.
Granulomatosis with polyangitis with mononeuritis multiplex-immunosuppressives playing a double-edged sword
TLDR
A 52-year-old female was diagnosed with rheumatoid arthritis and was on methotrexate and prednisolone when she developed fever, cough, hemoptysis, and cavitary lesion on chest skiagram, which confirmed the diagnosis of granulomatosis with polyangitis (GPA).
Granulomatosis with polyangiitis (Wegener's granulomatosis) with hard palate and bronchial perforations treated with rituximab - a case report.
TLDR
A 57-year-old woman suffering from granulomatosis with polyangiitis, who in the seventh months of immunosuppressive treatment (cyclophosphamide) progressed with new pulmonary changes and perforations of the hard palate and bronchi, is the first report of GPA refractory to cycloph phosphamide complicated by palatal and bronchial perforation.
Orbital manifestations of granulomatosis with polyangiitis: 12-year experience in Mexico City
TLDR
Ophthalmologists should consider this rare disease as a differential diagnosis of orbital tumors, as it may have different clinical manifestations, even in non-Caucasian population.
Thoracic manifestations of vasculitis
TLDR
The vasculitides encompass a disparate group of symptomatically and radiologically diverse conditions associated with an inflammatory and destructive process affecting the blood vessels that may represent diffuse alveolar haemorrhage.
...
...

References

SHOWING 1-5 OF 5 REFERENCES
ANCA disease: where is this field heading?
  • R. Falk, J. Jennette
  • Biology, Medicine
    Journal of the American Society of Nephrology : JASN
  • 2010
TLDR
The immunopathogenic effects of myeloperoxidase and proteinase 3 antibodies are well established, and good mechanisms for initiation of disease are starting to emerge, particularly the role of autoantigen complementarity.
Nomenclature of systemic vasculitides. Proposal of an international consensus conference.
The following are some of the conclusions and proposals made at the Chapel Hill Consensus Conference on the Nomenclature of Systemic Vasculitis. 1. Although not a prerequisite component of the
Wegener's granulomatosis.