Glioneuroma associated with colobomatous dysplasia of the anterior uvea and retina. A case simulating medulloepithelioma.

@article{Kivel1989GlioneuromaAW,
  title={Glioneuroma associated with colobomatous dysplasia of the anterior uvea and retina. A case simulating medulloepithelioma.},
  author={Tero T. Kivel{\"a} and L Kauniskangas and Pentti Miettinen and Ahti Tarkkanen},
  journal={Ophthalmology},
  year={1989},
  volume={96 12},
  pages={
          1799-808
        }
}
The left eye of an otherwise healthy child was enucleated at the age of 2 months because of an enlarging mass involving the temporal iris, ciliary body, and anterior retina. The initial histopathologic diagnosis was malignant medulloepithelioma with orbital extension. Closer study revealed a superotemporal chorioretinal and ciliary body coloboma; dysplasia of the adjacent retina; a glioneuromatous mass replacing the temporal ciliary body, chamber angle structures, and iris and extending through… 
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