Follow-up study of subunit c of mitochondrial ATP synthase (SCMAS) in Batten disease and in unrelated lysosomal disorders

@article{Elleder1997FollowupSO,
  title={Follow-up study of subunit c of mitochondrial ATP synthase (SCMAS) in Batten disease and in unrelated lysosomal disorders},
  author={Milan Elleder and Jitka Sokolov{\'a} and Martin Hřeb{\'i}{\vc}ek},
  journal={Acta Neuropathologica},
  year={1997},
  volume={93},
  pages={379-390}
}
Immunohistochemical and biochemical studies of subunit c of mitochondrial ATP synthase (SCMAS) storage were carried out in neuronal ceroid lipofuscinosis (NCL) and in a series of unrelated inherited and acquired lysosomal disorders. In the NCL group, represented by the late infantile, early juvenile and juvenile types, SCMAS storage was generalized neurovisceral, with considerable difference in the visceral storage pattern between the types. In late infantile NCL the SCMAS storage was intensive… CONTINUE READING

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