Features of Alagille syndrome in 92 patients: frequency and relation to prognosis.

Abstract

We have studied 92 patients with Alagille syndrome (AGS) to determine the frequency of clinical manifestations and to correlate the clinical findings with outcome. Liver biopsy specimens showed paucity of the interlobular ducts in 85% of patients. Cholestasis was seen in 96%, cardiac murmur in 97%, butterfly vertebrae in 51%, posterior embryotoxon in 78… (More)

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@article{Emerick1999FeaturesOA, title={Features of Alagille syndrome in 92 patients: frequency and relation to prognosis.}, author={Karan McBride Emerick and Emily Rand and Elizabeth Goldmuntz and Ingela Krantz and Nancy B. Spinner and David A. Piccoli}, journal={Hepatology}, year={1999}, volume={29 3}, pages={822-9} }